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Cadernos de Pós-Graduação em Distúrbios do Desenvolvimento

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MURRAY, Ana Cristina de Sousa et al. Instrumentation and evaluation of measurements of mip and mep in the pulmonary function of people with Duchenne muscular dystrophy: a review. Cad. Pós-Grad. Distúrb. Desenvolv. [online]. 2021, vol.21, n.1, pp. 109-128. ISSN 1519-0307.

CONTEXTUALIZATION: the decrease in pulmonary function in people with Duchenne muscular dystrophy (DMD) contributes to a significant morbidity due to the progressive weakness of the respiratory muscles. The characterization of respiratory function of this population is well-described worldwide, using pulmonary function tests with specific instruments that include measurements of maximal respiratory pressures. The assessment and measurement of these pressures are of clinical relevance and necessary for therapeutic adequacy. As there is no standardization in the protocol of the equipment to be used, there is great variability between the evaluations. In this article, we demonstrate this and suggest following the protocol already developed by European and American associations and the Brazilian Consensuson Spirometry, creating a standard for the clinical evaluation of people with DMD. OBJECTIVES: identifying and characterizing the main criteria and instruments for evaluating maximum inspiratory pressure (MIP) and maximum expiratory pressure (MEP) in pulmonary functions of people with DMD. METHOD: this study is an analytical bibliographic review of scientific articles and was subdivided into four phases: collection, selection, tabulation of data and characterization of evaluation instruments. The terms used in Portuguese were: distrofia muscular de Duchenne e/ou pressões respiratórias máximas e/ou faixa etária. In English: Duchenne muscular dystrophy and/or maximal respiratory pressure and/or age group. Inclusion criteria was used to select the articles. RESULTS: the results were tabulated according to the number of patients, objectives, inclusion criteria and evaluation instruments. CONCLUSION: the objectives were achieved, there was not a single standardization among the articles studied; only one used the evaluation criteria for people with neuromuscular diseases described by the American Thoracic Society (ATS), and none followed a standardization of the instrument. However, the evaluations that were done, which were developed with standards for non-sick people, are still options for correlating a standard for assessing respiratory function in patients with DMD.

Keywords : Duchenne muscular dystrophy; Maximal respiratory pressure; Age group; Pulmonary function; Respiratory system.

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